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BSC SEM 4 UNIT 1 PATHOLOGY 2 & GENETICS.

UNIT 1 Introduction:

🌱 Introduction to Genetics

🔬 What is Genetics?

Genetics is the branch of biology that deals with the study of genes, heredity, and variation in living organisms. It explains how traits and conditions are passed from one generation to the next through DNA (Deoxyribonucleic Acid).


📘 Key Terms in Genetics

TermMeaning
GeneBasic unit of heredity that carries instructions for making proteins.
ChromosomeA structure made of DNA and proteins found in the nucleus of cells. Humans have 46 chromosomes (23 pairs).
DNAMolecule that carries genetic information.
GenomeComplete set of genes in an organism.
MutationA change in the DNA sequence that can affect how genes work.

🧬 Branches of Genetics

  1. Classical Genetics – Study of inheritance of traits (Mendelian Genetics).
  2. Molecular Genetics – Study of structure and function of genes at a molecular level.
  3. Population Genetics – Study of genetic variation in populations.
  4. Medical Genetics – Study of genetic causes of human disease.
  5. Genomic Medicine – Use of genomic information for diagnosis, treatment, and prevention of diseases.

🧑‍⚕️ Genetic Nursing: A Modern Specialty

🔍 What is Genetic Nursing?

Genetic Nursing involves applying genetic and genomic information in healthcare to:

  • Identify individuals at risk for genetic conditions.
  • Support genetic screening and testing.
  • Provide genetic counseling.
  • Participate in the prevention and management of hereditary diseases.

🩺 Role of a Genetic Nurse

RoleDescription
AssessmentCollect family history (pedigree), recognize hereditary patterns.
EducationEducate patients and families on inheritance, genetic risks, and testing.
CounselingOffer support and information for decision-making regarding genetic testing and reproductive options.
Care PlanningCoordinate with genetic counselors, doctors, and labs to plan personalized care.
AdvocacyProtect patient rights and confidentiality in genetic issues.

🧪 Genetic Testing in Nursing Practice

  • Carrier Testing – To find out if a person carries a gene for a genetic disorder.
  • Predictive Testing – For asymptomatic individuals at risk (e.g., BRCA gene for breast cancer).
  • Prenatal Testing – During pregnancy to assess risk of genetic disorders in fetus.
  • Newborn Screening – Mandatory screening for inherited disorders at birth.

🧑‍⚕️💡 Why Genetic Nursing is Important in Today’s Healthcare

  1. Early Detection of Genetic Disorders – Helps initiate timely interventions.
  2. Personalized Medicine – Treatment plans based on individual genetic makeup.
  3. Disease Prevention – Lifestyle changes and monitoring in genetically at-risk individuals.
  4. Ethical & Emotional Support – Patients need counseling for genetic decisions.
  5. Interdisciplinary Collaboration – Nurses are vital in the genetic healthcare team.

⚖️ Ethical & Legal Issues in Genetic Nursing

IssueExplanation
ConfidentialityGenetic information must be protected.
Informed ConsentPatients must understand risks/benefits before genetic testing.
DiscriminationGuard against misuse of genetic data (insurance, employment).
AutonomyRespect for patients’ rights in making genetic decisions.

🏥 Applications of Genetics in Nursing Fields

  • Oncology: Genetic testing for breast, ovarian, colon cancers.
  • Pediatrics: Management of inherited disorders like cystic fibrosis or thalassemia.
  • Obstetrics: Prenatal diagnosis of genetic conditions.
  • Neurology: Genetic role in diseases like Huntington’s or Alzheimer’s.
  • Psychiatry: Studying heritability of mental illnesses.

🎓 Education and Training in Genetic Nursing

  • Courses in genetics/genomics, bioethics, and counseling.
  • Continued education through workshops, conferences, and certification programs.
  • Collaboration with genetic counselors, molecular biologists, and clinicians.

📈 Future of Genetic Nursing

  • Expansion due to advances in genomic medicine and gene therapy.
  • Involvement in genome editing (e.g., CRISPR), pharmacogenomics, and precision health.
  • Demand for nurse geneticists and genetic nurse educators will rise.

🧬 Practical Applications of Genetics in Nursing

Genetics is no longer just a theoretical subject — it plays a crucial role in day-to-day nursing care. Nurses use genetics to assess risk, educate patients, make referrals, and provide individualized care based on a person’s genetic profile.


🩺 1. Genetic Risk Assessment

  • Nurses collect detailed family histories (3 generations) to identify inherited diseases.
  • Helps in early detection of diseases like cancer, diabetes, hypertension, etc.
  • Example: If a woman’s mother and sister had breast cancer, the nurse may recommend BRCA gene screening.

🧾 2. Patient Education and Counseling

  • Nurses educate patients about:
    • Hereditary conditions.
    • The meaning of genetic test results.
    • Lifestyle modifications for genetically inherited risks.
  • Example: Teaching a patient with a family history of thalassemia about carrier screening before marriage.

🧪 3. Facilitating Genetic Testing

  • Nurses play a key role in:
    • Preparing patients for genetic tests.
    • Explaining the process, benefits, and limitations.
    • Ensuring informed consent.
  • Example: Assisting in prenatal screening for Down syndrome during antenatal checkups.

📋 4. Incorporating Genetics into Nursing Care Plans

  • Nursing care is personalized based on genetic predispositions.
  • Nurses monitor for specific symptoms or complications based on known genetic risks.
  • Example: A patient with sickle cell anemia needs hydration and oxygenation protocols carefully maintained.

🤝 5. Referral and Collaboration

  • Nurses coordinate with genetic counselors, physicians, and specialists.
  • Refer patients who need further genetic evaluation or support.
  • Example: A couple with repeated miscarriages referred for chromosomal analysis.

🧫 6. Newborn Screening and Early Intervention

  • Nurses assist in screening newborns for inherited metabolic and genetic disorders.
  • Prompt action can prevent disability or death.
  • Example: Early detection of phenylketonuria (PKU) or congenital hypothyroidism in newborns.

💊 7. Pharmacogenomics in Medication Management

  • Nurses are involved in administering drugs based on genetic compatibility.
  • Certain drugs work differently based on genetic variations.
  • Example: A patient with a genetic variation may need a lower dose of warfarin to prevent bleeding.

🧠 8. Managing Genetic Disorders

  • Nurses provide long-term care and support for patients with:
    • Thalassemia
    • Hemophilia
    • Muscular dystrophy
    • Cystic fibrosis
  • Includes psychological support, nutritional counseling, infection prevention, etc.

⚖️ 9. Ethical and Legal Responsibilities

  • Protect patients’ genetic privacy and prevent discrimination.
  • Educate patients about their rights.
  • Uphold confidentiality in sharing genetic information.

🧠 10. Psychosocial Support and Coping

  • Genetic diseases can lead to anxiety, guilt, or stress.
  • Nurses provide emotional support and guide families in coping with diagnosis or uncertainty.
  • Example: Supporting parents after a prenatal diagnosis of a genetic syndrome.

🏥 11. Community Health and Genetic Awareness

  • Conduct awareness programs in schools and rural areas about:
    • Hereditary disorders.
    • Consanguineous marriage risks.
    • Importance of premarital or prenatal screening.

✅ Summary Table

ApplicationRole of NurseExample
Risk AssessmentTake family historyCancer screening
EducationExplain inheritanceSickle cell traits
Genetic TestingPrepare patient, consentBRCA, CF testing
Care PlanningIndividualized careHemophilia precautions
ReferralGenetic counselorRecurrent abortions
Newborn ScreeningEarly detectionHypothyroidism
PharmacogenomicsSafe drug dosageWarfarin adjustment
Genetic Disorder CareLong-term managementThalassemia care
EthicsConfidentiality, consentGene test privacy
Psychosocial SupportEmotional careCoping with disability
Community ProgramsHealth teachingAwareness on cousin marriages

🧬 Impact of Genetic Conditions on Families

A genetic condition doesn’t only affect the individual diagnosed — it has a wide-ranging impact on the entire family system, including emotional, psychological, social, financial, and ethical dimensions. Nurses play a vital role in supporting families through these challenges.


🧠 1. Emotional Impact

  • Families may experience shock, grief, guilt, fear, sadness, and anxiety after diagnosis.
  • Parents may blame themselves for passing on a genetic condition.
  • Siblings may feel neglected, jealous, or worried about their own genetic risks.

Example: Parents of a child with Duchenne Muscular Dystrophy may go through stages of denial and depression.


🫂 2. Psychological Stress

  • Ongoing care, future uncertainty, and witnessing a loved one’s suffering can lead to:
    • Chronic stress
    • Depression
    • Caregiver burnout
    • Post-traumatic stress

Example: A mother caring for a child with autism may face social isolation and chronic fatigue.


🧾 3. Financial Burden

  • High cost of:
    • Genetic testing
    • Specialized treatment and therapy
    • Supportive devices (e.g., braces, wheelchairs)
    • Frequent hospital visits
  • Families may face loss of income if a parent becomes a full-time caregiver.

Example: Treating thalassemia requires lifelong blood transfusions and iron chelation, which can be economically draining.


🧬 4. Genetic Guilt and Fear

  • Family members may worry about:
    • Passing the condition to their children.
    • Their own genetic status (asymptomatic carriers).
  • May lead to fear of future pregnancies, avoidance of marriage, or emotional withdrawal.

Example: A woman who carries a BRCA mutation might fear having children or struggle with major decisions like preventive surgery.


🏠 5. Social Impact

  • Families may face stigma, discrimination, or misunderstanding in their communities.
  • Cultural beliefs or lack of awareness may result in isolation or judgment.

Example: In some cultures, families of children with intellectual disabilities may be socially excluded or blamed.


👨‍👩‍👧‍👦 6. Family Relationship Strain

  • Increased caregiving demands may cause:
    • Strain in marital relationships
    • Sibling rivalry or guilt
    • Generational conflicts (blame from grandparents, etc.)

Example: Parents may argue over treatment decisions or one partner may feel unsupported.


⚖️ 7. Ethical and Reproductive Decisions

  • Families may face complex choices:
    • Whether to have more children.
    • Whether to pursue prenatal diagnosis or IVF with genetic selection.
  • May involve deep ethical, religious, or cultural conflicts.

Example: A couple who are both carriers of sickle cell may be torn about having a second child.


🩺 8. Need for Long-Term Care and Planning

  • Many genetic disorders are chronic or progressive.
  • Families need to:
    • Plan for long-term care, special education, future guardianship.
    • Adjust routines, living environments, or even move closer to medical facilities.

Example: A child with cerebral palsy may need a wheelchair-accessible home and special schooling.


🧠 9. Impact on Siblings

  • Healthy siblings may feel:
    • Jealousy over attention given to affected sibling.
    • Guilt for being healthy.
    • Fear of inheriting the condition or passing it on.

Example: A teen whose brother has Down syndrome may struggle with peer pressure and social embarrassment.


🤝 10. Support Systems and Coping

  • Families may benefit from:
    • Genetic counseling
    • Psychological therapy
    • Support groups
    • Financial aid schemes
  • Positive coping can strengthen family bonds and resilience.

✅ Summary Table

Impact AreaDescriptionExample
EmotionalGrief, fear, guiltParents of a disabled child
PsychologicalDepression, stressCaregiver burnout
FinancialHigh treatment costThalassemia management
Genetic GuiltInheritance anxietyBRCA mutation
SocialStigma, isolationAutism or epilepsy
RelationshipMarital strainConflict over decisions
Reproductive EthicsPrenatal testing dilemmasCarrier couples
Long-Term PlanningHome/school adaptationsCerebral palsy
SiblingsJealousy, confusionFeel neglected
CopingCounseling, supportResilience through therapy

👩‍⚕️ Role of Nurse in Supporting Families:

  • Provide empathetic counseling and education
  • Refer to genetic counselors, support groups, and social workers
  • Encourage open family communication
  • Respect cultural, religious, and personal beliefs
  • Advocate for rights and access to care

🔬 Review of Cellular Division: Mitosis

🌱 What is Cell Division?

Cell division is the process by which a single parent cell divides to form two daughter cells. It is essential for growth, tissue repair, and asexual reproduction.

There are two major types:

  1. Mitosis – For growth and repair (body cells).
  2. Meiosis – For reproduction (gametes/sex cells).

🔁 Mitosis – Definition

Mitosis is the process by which a diploid somatic cell (2n) divides to produce two genetically identical daughter cells, each with the same number of chromosomes as the parent cell.

  • Occurs in somatic (body) cells
  • Helps in growth, healing, and cell replacement

🧬 Phases of Mitosis

Mitosis occurs in 5 phases (after interphase):

1. 🧼 Interphase (Preparation Phase – not part of mitosis)

  • The cell grows and prepares for division.
  • DNA replication occurs (chromosomes double).
  • The cell has 2 full sets of chromosomes by the end.

2. 🌟 Prophase

  • Chromosomes condense and become visible.
  • Nuclear envelope begins to break down.
  • Spindle fibers begin to form from centrioles.
  • Each chromosome is made of two sister chromatids joined at a centromere.

3. 📐 Metaphase

  • Chromosomes line up at the metaphase plate (center of the cell).
  • Spindle fibers attach to centromeres of chromosomes.
  • This is the best phase to study chromosomes microscopically.

4. ✂️ Anaphase

  • Sister chromatids separate and are pulled to opposite poles by the spindle fibers.
  • Each chromatid becomes an individual chromosome.

5. 🧱 Telophase

  • Chromosomes reach opposite poles.
  • New nuclear membranes form around each set.
  • Chromosomes start to uncoil back into chromatin.
  • Spindle fibers disappear.

6. 🍽️ Cytokinesis (Final Division of Cytoplasm)

  • The cell membrane pinches in to form two separate daughter cells.
  • Each has an identical nucleus and same number of chromosomes as the parent.

📊 Summary of Mitosis

StageKey Events
InterphaseDNA replication, cell growth
ProphaseChromosomes visible, spindle forms
MetaphaseChromosomes align in center
AnaphaseSister chromatids pulled apart
TelophaseTwo nuclei reform
CytokinesisCytoplasm divides into 2 cells

🧠 Characteristics of Mitosis

FeatureDetails
Type of CellSomatic (body) cells
No. of Divisions1
No. of Daughter Cells2
Chromosome NumberSame as parent (Diploid – 2n)
Genetic IdentityIdentical to parent cell
FunctionGrowth, repair, regeneration

🧑‍⚕️ Relevance of Mitosis in Nursing

ApplicationExample
Wound HealingSkin cells divide to repair cuts
Tissue GrowthChildren’s height increases through cell multiplication
Cancer UnderstandingUncontrolled mitosis leads to tumors
Stem Cell TherapyMitosis helps in regenerating tissues
RegenerationReplacement of damaged blood cells, liver cells, etc.

⚠️ Clinical Insight: Mitosis and Cancer

  • In cancer, mitosis becomes uncontrolled, leading to abnormal cell growth.
  • Nurses need to understand mitosis for cancer education, chemotherapy mechanisms, and cell cycle-targeted drugs.

🧬 Review of Cellular Division: Meiosis

🌱 What is Meiosis?

Meiosis is a special type of cell division that occurs only in reproductive (germ) cells (i.e., sperm and ova). It reduces the chromosome number by half, producing four genetically unique haploid cells.

🧾 Purpose of Meiosis:

  • Formation of gametes (egg and sperm).
  • Maintains chromosome number across generations.
  • Introduces genetic variation in offspring.

🔁 Basic Concept

FeatureMeiosisMitosis
Cell TypeGerm cellsSomatic cells
No. of Divisions21
Daughter Cells42
Chromosome NumberHaploid (n)Diploid (2n)
Genetic IdentityDifferentIdentical
PurposeReproductionGrowth and repair

🔬 Stages of Meiosis

Meiosis consists of two successive divisions:

  1. Meiosis I – Reduction Division
  2. Meiosis II – Similar to mitosis

🧪 Meiosis I: Reduction Division

Reduces chromosome number from diploid (2n) to haploid (n).

1. Prophase I

  • Chromosomes condense.
  • Homologous chromosomes pair up (synapsis).
  • Crossing over occurs → exchange of genetic material → genetic variation.
  • Nuclear membrane dissolves, spindle fibers form.

2. Metaphase I

  • Homologous pairs align at the metaphase plate.
  • Random alignment contributes to genetic variation.

3. Anaphase I

  • Homologous chromosomes separate (sister chromatids remain together).
  • Pulled to opposite poles.

4. Telophase I and Cytokinesis

  • Two haploid cells form (each with half the number of chromosomes).
  • Each chromosome still has two chromatids.

🧪 Meiosis II: Equational Division

Similar to mitosis, separates sister chromatids.

1. Prophase II

  • Chromosomes condense in both haploid cells.
  • Spindle forms.

2. Metaphase II

  • Chromosomes align at the equator.

3. Anaphase II

  • Sister chromatids separate and move to opposite poles.

4. Telophase II and Cytokinesis

  • Nuclear membranes form.
  • Cytoplasm divides.
  • Four genetically distinct haploid cells are formed.

📊 Summary of Meiosis

StageKey Features
Prophase IHomologous chromosomes pair and cross over
Metaphase IHomologous pairs align at center
Anaphase IHomologous chromosomes separate
Telophase ITwo haploid cells form
Meiosis IISister chromatids separate like mitosis
End ResultFour haploid gametes

🧬 Significance of Meiosis

  1. Reduces chromosome number by half.
  2. 🧠 Maintains species stability during sexual reproduction.
  3. 🔁 Promotes genetic variation (crossing over, independent assortment).
  4. 💫 Basis of heredity – combines genes from both parents.

👩‍⚕️ Importance of Meiosis in Nursing Practice

RelevanceExample
Reproductive HealthUnderstanding fertilization, ovulation
Genetic DisordersDown syndrome (non-disjunction in meiosis)
Prenatal ScreeningDetecting chromosomal abnormalities
CounselingExplaining inheritance patterns in genetic counseling
InfertilityUnderstanding meiotic failure in gamete formation

⚠️ Clinical Insight: Errors in Meiosis

ErrorOutcome
Non-disjunctionFailure of chromosomes to separate
Trisomy 21Down Syndrome (extra chromosome 21)
Turner Syndrome (XO)Missing X chromosome in females
Klinefelter Syndrome (XXY)Extra X in males

🎯 Recap – Differences between Mitosis & Meiosis

FeatureMitosisMeiosis
Cell TypeSomaticGerm
No. of Cells24
ChromosomeDiploidHaploid
Genetic IdentityIdenticalDifferent
PurposeGrowth/RepairReproduction

🧬 Characteristics and Structure of Genes


🌱 What is a Gene?

A gene is a specific segment of DNA (deoxyribonucleic acid) that contains the instructions to make a particular protein or regulate a function. Genes are the basic units of heredity.


🧬 Structure of a Gene

Genes are part of the DNA located on chromosomes. The structure of a gene includes:

1. 🧾 Promoter Region

  • Located at the start of the gene.
  • Acts like a “switch” to turn gene on or off.
  • Helps RNA polymerase bind and start transcription.

2. 🧬 Coding Region (Exons and Introns)

  • Exons: Contain actual coding information to make a protein.
  • Introns: Non-coding sequences between exons (removed during RNA processing).

3. 🧪 Terminator Region

  • Signals the end of the gene.
  • Tells transcription machinery to stop copying DNA to RNA.

🔁 Gene to Protein: The Central Dogma

DNA → (Transcription) → RNA → (Translation) → Protein

This process ensures that the instructions in genes result in the production of proteins that carry out cellular functions.


🧠 Characteristics of Genes

CharacteristicDescription
Heredity UnitGenes are passed from parents to offspring and determine traits (like eye color, blood type).
Specific LocationEach gene is located at a specific place (locus) on a chromosome.
Paired FormExist in pairs – one from each parent. Alternate forms are called alleles.
ExpressionGenes can be dominant (expressed) or recessive (masked).
MutabilityGenes can undergo mutation – permanent change in DNA sequence.
FunctionalityEach gene has a specific function – often to code for a protein.
Universal CodeThe genetic code is nearly universal across all living organisms.
RegulationGene expression is regulated depending on the needs of the cell.
ReplicationGenes are copied during cell division, ensuring genetic continuity.

🔍 Important Gene Terms

TermMeaning
AlleleDifferent forms of the same gene (e.g., A and a for blood group).
GenotypeThe genetic makeup of an organism (e.g., Aa, AA).
PhenotypeThe physical expression of the genotype (e.g., eye color).
HomozygousSame alleles (e.g., AA or aa).
HeterozygousDifferent alleles (e.g., Aa).
MutationChange in the gene sequence that may cause disease or variation.

🧬 Functions of Genes

  1. ✅ Code for proteins that perform cellular activities.
  2. 🔁 Inherit traits from parents (e.g., skin color, height).
  3. 🧠 Control development and growth.
  4. 🩺 Influence health and disease (e.g., BRCA1 in breast cancer).
  5. 🧫 Regulate metabolism, immune response, and repair.

🔬 Example: Structure of the Hemoglobin Gene

  • Found on Chromosome 11.
  • Has exons (coding for α or β chains of hemoglobin).
  • Mutations in this gene may cause thalassemia or sickle cell anemia.

👩‍⚕️ Importance of Gene Knowledge in Nursing

AreaApplication
Genetic CounselingExplaining hereditary risks (e.g., thalassemia carrier status).
Prenatal CareUnderstanding fetal development and congenital conditions.
PharmacogenomicsPersonalized drugs based on genetic makeup.
Cancer CareBRCA1/2 gene testing in breast cancer.
Patient EducationTeaching families about inherited conditions.

🧬 Chromosomes and Sex Determination


🧾 What are Chromosomes?

Chromosomes are thread-like structures made of DNA and proteins, found in the nucleus of every cell. They carry genes, which determine traits and control bodily functions.

  • Humans have 46 chromosomes (23 pairs):
    • 22 pairs of autosomes (non-sex chromosomes)
    • 1 pair of sex chromosomes (X and Y)

👶 Sex Chromosomes and Gender Determination

🧬 Sex Chromosomes:

  • Females have XX sex chromosomes.
  • Males have XY sex chromosomes.
GenderSex Chromosomes
FemaleXX
MaleXY

🧫 How is Sex Determined?

Sex is determined at fertilization, depending on whether the sperm contributes an X or Y chromosome.

ParentChromosome Given
Mother (egg)Always gives X
Father (sperm)Gives X or Y
Sperm ContributesResulting Sex
X chromosomeXX = Female
Y chromosomeXY = Male

🔍 Therefore, the father’s sperm decides the sex of the child.


🧬 Genetic Combinations and Inheritance

CombinationResult
X (egg) + X (sperm)XX → Girl
X (egg) + Y (sperm)XY → Boy

🌟 Function of Sex Chromosomes

ChromosomeFunction
X ChromosomeCarries genes for many bodily functions and female development.
Y ChromosomeHas genes that determine male traits, especially the SRY gene (Sex-determining Region Y) which triggers male development.

⚠️ Disorders of Sex Chromosomes

Sometimes abnormalities in sex chromosomes lead to genetic disorders:

ConditionChromosomal PatternFeatures
Turner SyndromeXO (Only one X, no Y)Female with short stature, infertility
Klinefelter SyndromeXXYMale with learning issues, infertility
Triple X SyndromeXXXUsually normal female, may have mild symptoms
XYY SyndromeXYYMale, often taller than average, possible learning issues

🧑‍⚕️ Importance of Understanding Sex Determination in Nursing

AreaApplication
Prenatal CounselingExplaining fetal development and potential disorders.
Genetic TestingInterpreting chromosomal studies (e.g., karyotyping).
Ethical EducationEducating families that the father determines the baby’s sex, not the mother.
Congenital DisordersEarly detection and care planning for chromosomal abnormalities.
Reproductive HealthAdvising on inheritance, family planning, and infertility.

💡 Key Points to Remember

  • Humans have 23 pairs of chromosomes: 22 autosomes + 1 pair of sex chromosomes.
  • Sex is determined at fertilization.
  • Sperm (X or Y) decides if the child will be male or female.
  • Sex chromosome abnormalities can lead to developmental or fertility issues.
  • Nurses play a vital role in counseling, testing, and supporting families affected by genetic or chromosomal conditions.

🧬 Chromosomal Aberrations (Chromosomal Disorders)

🧾 Definition

Chromosomal aberrations are structural or numerical changes in chromosomes that can lead to congenital abnormalities, genetic disorders, or developmental problems.

They can be:

  • Numerical aberrations – change in the number of chromosomes.
  • Structural aberrations – alteration in the structure of chromosomes.

🧮 1. Numerical Chromosomal Aberrations

These occur when a person has more or fewer chromosomes than the normal 46.

🔢 Types:

TypeDescription
AneuploidyGain or loss of a single chromosome (e.g., 45 or 47 chromosomes)
PolyploidyGain of an entire set of chromosomes (e.g., 69 chromosomes) – often not compatible with life

⚠️ Common Numerical Disorders

DisorderChromosomeFeatures
Down SyndromeTrisomy 21 (47 chromosomes)Intellectual disability, flat face, heart defects
Turner SyndromeXO (Only one X chromosome)Female, short stature, infertility
Klinefelter SyndromeXXY (extra X in males)Male, tall, infertile, mild learning disability
Patau SyndromeTrisomy 13Severe intellectual disability, cleft lip/palate
Edwards SyndromeTrisomy 18Growth delay, heart defects, clenched fists

🧬 2. Structural Chromosomal Aberrations

These occur when the structure of one or more chromosomes is altered.

🧪 Types:

TypeDescriptionExample
DeletionA part of a chromosome is missingCri-du-chat syndrome (deletion on chromosome 5)
DuplicationA segment is copied twiceSome forms of developmental delay
InversionA piece of chromosome breaks and reattaches in reverse orderMay be silent or cause miscarriage
TranslocationA piece of one chromosome attaches to anotherDown syndrome (in rare cases – Robertsonian translocation)
Ring ChromosomeEnds of a chromosome join to form a ringMay cause growth or learning issues

🧑‍⚕️ Causes of Chromosomal Aberrations

CauseExample
Errors during meiosisNon-disjunction (failure to separate chromosomes)
Radiation exposureX-rays, radioactive materials
ChemicalsMutagenic agents, e.g., benzene
Maternal age > 35Higher risk of trisomies like Down syndrome
Viral infections during pregnancyMay interfere with normal cell division

🧠 Signs and Symptoms of Chromosomal Disorders

  • Developmental delay
  • Intellectual disability
  • Physical deformities
  • Congenital heart defects
  • Abnormal facial features
  • Fertility issues

👩‍⚕️ Nursing Implications and Roles

AreaNurse’s Role
Genetic CounselingEducate parents about hereditary risk and testing
Prenatal ScreeningAssist in ultrasound, blood tests, amniocentesis
Care PlanningHelp in managing children with special needs
Support and AdvocacyEmotional and social support for families
Health EducationRaise awareness about maternal health and genetic risks

📊 Summary Table

TypeSubtypeExampleChromosomes
NumericalTrisomyDown Syndrome47 (extra chromosome 21)
MonosomyTurner Syndrome45 (missing X)
StructuralDeletionCri-du-chatPartial deletion of chromosome 5
TranslocationRobertsonian Down SyndromeChromosome 14+21 fusion
InversionMay be asymptomatic or cause miscarriage

🎯 Key Takeaways

  • Chromosomal aberrations can affect physical, intellectual, and reproductive health.
  • Can be detected through karyotyping, FISH, or prenatal screening.
  • Nurses must be aware of their causes, implications, and how to support affected individuals and families.

🧬 Patterns of Inheritance


🧾 What is Inheritance?

Inheritance refers to the way genetic traits and disorders are passed from parents to offspring through genes. The pattern depends on the type of gene involved (dominant, recessive, autosomal, or sex-linked).


🌳 Basic Terms to Know

TermMeaning
GeneSegment of DNA that controls a trait.
AlleleVariations of a gene (e.g., A or a).
GenotypeGenetic makeup (e.g., AA, Aa, aa).
PhenotypeObservable trait (e.g., blood type, hair color).
HomozygousTwo identical alleles (AA or aa).
HeterozygousTwo different alleles (Aa).

📚 Main Patterns of Inheritance

1️⃣ Autosomal Dominant Inheritance

  • Only one copy of the dominant gene (from either parent) is enough to show the trait.
  • Affected individuals have a 50% chance of passing it to offspring.
  • Occurs in every generation.

🧬 Examples: Huntington’s disease, Marfan syndrome, Familial hypercholesterolemia

GenotypePhenotype
AA or AaAffected
aaNormal

2️⃣ Autosomal Recessive Inheritance

  • Trait appears only when both alleles are defective.
  • Parents may be carriers (Aa) but not show the disease.
  • 25% chance of affected child if both parents are carriers.

🧬 Examples: Cystic fibrosis, Sickle cell anemia, Thalassemia, Tay-Sachs disease

GenotypePhenotype
aaAffected
AaCarrier
AANormal

3️⃣ X-linked Recessive Inheritance

  • Gene is located on the X chromosome.
  • Males (XY) are more commonly affected because they have only one X chromosome.
  • Females (XX) can be carriers or affected if both X chromosomes carry the gene.

🧬 Examples: Hemophilia A, Duchenne muscular dystrophy, Color blindness

Parent GenotypeOutcome
Carrier mother (XᴴX) + Normal father (XY)50% sons affected, 50% daughters carriers

4️⃣ X-linked Dominant Inheritance

  • A single defective gene on the X chromosome causes the disorder in both males and females.
  • Often more severe in males.
  • Affected fathers cannot pass it to sons, but all daughters will be affected.

🧬 Examples: Rett syndrome, Fragile X syndrome (can also behave as semi-dominant)


5️⃣ Y-linked Inheritance (Holandric)

  • Gene is on the Y chromosome → Only males are affected.
  • Passed from father to son.
  • Very rare.

🧬 Example: Y-linked hearing loss, Swyer syndrome


6️⃣ Mitochondrial Inheritance (Maternal Inheritance)

  • Genes inherited from mitochondria, which come only from the mother.
  • Both sons and daughters can be affected, but only mothers pass it on.

🧬 Examples: Leber’s hereditary optic neuropathy, mitochondrial myopathy


📊 Summary Table: Patterns of Inheritance

PatternChromosome InvolvedWho is AffectedTransmission
Autosomal DominantAutosomesMales & femalesAffected parent to child (50%)
Autosomal RecessiveAutosomesMales & femalesCarrier parents (25% affected)
X-linked RecessiveX chromosomeMostly malesCarrier mother to sons
X-linked DominantX chromosomeBoth sexesAffected father → all daughters
Y-linkedY chromosomeOnly malesFather to son
MitochondrialMitochondrial DNABoth sexesOnly through mother

🧑‍⚕️ Nursing Relevance and Application

AreaApplication
Genetic CounselingExplain risk of inheritance to parents.
Prenatal ScreeningIdentify inherited diseases (e.g., thalassemia).
Patient EducationTeach families about dominant/recessive traits.
Diagnosis SupportUnderstand family history for risk factors.
Ethical PracticeGuide patients in informed decisions.

🌿 Mendelian Theory of Inheritance


👨‍🔬 Who was Gregor Mendel?

  • Gregor Johann Mendel was an Austrian monk and botanist.
  • Known as the “Father of Genetics”.
  • Conducted experiments on pea plants (Pisum sativum) in the mid-1800s.
  • Discovered how traits are passed from one generation to the next.

🌱 Mendel’s Experiments:

  • Used pea plants because they:
    • Had clear, contrasting traits (e.g., tall vs. dwarf).
    • Could be easily self- or cross-pollinated.
  • Studied 7 traits, such as:
    • Flower color
    • Plant height
    • Seed shape

📚 Mendel’s Laws of Inheritance

Mendel proposed three major laws based on his experiments:


1️⃣ Law of Segregation (First Law)

“Each individual has two alleles for a trait, and these alleles segregate (separate) during gamete formation.”

  • Every trait is controlled by a pair of alleles (one from each parent).
  • During meiosis, the two alleles separate so that each gamete gets only one allele.
  • After fertilization, the new organism gets one allele from each parent.

🧬 Example:
A plant with alleles Tt (Tall, short) will produce two types of gametes: T and t.


2️⃣ Law of Independent Assortment (Second Law)

“Genes for different traits are inherited independently of each other.”

  • The inheritance of one trait (e.g., flower color) does not affect the inheritance of another (e.g., seed shape).
  • Occurs during di-hybrid crosses (e.g., RrYy).

🧪 Example:
Round yellow seeds (RrYy) may produce offspring with all combinations: Round-Green, Wrinkled-Yellow, etc.


3️⃣ Law of Dominance (Third Law)

“When two different alleles are present, one (dominant) allele masks the effect of the other (recessive).”

  • The dominant allele expresses itself even in the presence of a recessive allele.
  • The recessive trait only appears when both alleles are recessive.

🧬 Example:
In a cross between Tall (TT) and Dwarf (tt), all offspring (Tt) are Tall, because T is dominant over t.


🧬 Key Genetic Terms (Quick Recap)

TermMeaning
GeneUnit of heredity
AlleleAlternative form of a gene (T or t)
DominantExpressed trait (T)
RecessiveHidden when dominant is present (t)
HomozygousSame alleles (TT or tt)
HeterozygousDifferent alleles (Tt)
GenotypeGenetic makeup (e.g., Tt)
PhenotypePhysical appearance (e.g., tall)

🧪 Monohybrid Cross (Single Trait)

Cross: TT (Tall) × tt (Dwarf)

Parent GenotypesOffspring GenotypeOffspring Phenotype
TT × ttAll TtAll Tall (100%)

🧬 Dihybrid Cross (Two Traits)

Cross: RrYy × RrYy

(R = Round, r = Wrinkled, Y = Yellow, y = Green)

Outcome9:3:3:1 Phenotypic Ratio
9 Round Yellow
3 Round Green
3 Wrinkled Yellow
1 Wrinkled Green

🧠 Nursing Relevance of Mendelian Genetics

AreaApplication
Genetic DisordersUnderstanding recessive/dominant inheritance (e.g., sickle cell anemia, hemophilia)
Genetic CounselingHelping parents understand risk of inherited conditions
Prenatal TestingAdvising on carrier screening and risk assessment
PharmacogeneticsHow inherited traits affect drug metabolism
Patient EducationExplaining inheritance in simple terms to families

🎯 Key Takeaways

  • Traits are inherited through alleles, which come in pairs.
  • Dominant alleles mask recessive ones.
  • Traits sort independently unless they’re linked.
  • These laws help explain heredity, variation, and risk of genetic disorders.

🧬 Multiple Alleles and Blood Groups


🔁 What Are Multiple Alleles?

  • Multiple alleles refer to a gene that exists in more than two alternative forms (alleles), although any individual inherits only two (one from each parent).
  • This concept expands Mendel’s work, which was based on only two alleles (dominant and recessive).

🧠 Key Point:
Multiple alleles = more than two types of a gene existing in the population, but an individual has only two at a time.


🩸 Classic Example: ABO Blood Group System

The ABO blood group system is controlled by a single gene (I) with three alleles:

AlleleDescription
IᴬCodes for A antigen on RBC
IᴮCodes for B antigen on RBC
iNo antigen (O type)

🔬 Genotypes and Blood Group Types

GenotypeBlood GroupAntigen on RBCAntibodies in Plasma
IᴬIᴬ or IᴬiAA antigenAnti-B
IᴮIᴮ or IᴮiBB antigenAnti-A
IᴬIᴮABA & B antigensNone
iiONo antigenAnti-A & Anti-B

🧬 Important Genetic Features

  • Iᴬ and Iᴮ are co-dominant – both are expressed when present together (AB group).
  • i is recessive – only expressed in homozygous form (ii = O group).

🧑‍⚕️ Relevance to Nursing and Healthcare

AreaApplication
Blood TransfusionNurses must ensure compatible blood typing to avoid hemolytic reaction.
Organ TransplantationCompatibility is partially based on blood groups.
Maternal-Fetal HealthBlood group incompatibility (e.g., Rh factor) can lead to Erythroblastosis Fetalis.
Genetic CounselingHelps explain inheritance of blood groups and paternity testing.

💉 Blood Group Compatibility Chart

Recipient → <br> Donor ↓ABABO
A
B
AB (Universal Recipient)
O (Universal Donor)

📊 Punnett Square Example

Cross: Iᴬi × Iᴮi

Iᴮi
IᴬABA
iBO

🧬 Offspring Blood Group Possibilities:

  • A (25%)
  • B (25%)
  • AB (25%)
  • O (25%)

Summary of Key Points

  • Multiple alleles = More than 2 allele types in the population (e.g., Iᴬ, Iᴮ, i).
  • Blood type is determined by genotype combinations of these alleles.
  • Blood transfusion safety depends on blood group compatibility.
  • Nurses must understand blood typing for safe practice and patient education.

🧬 Sex-Linked Inheritance


🧾 Definition

Sex-linked inheritance refers to the inheritance of genes located on the sex chromosomes (X or Y). These genes are passed from parent to child based on the child’s sex (gender).

  • Humans have 23 pairs of chromosomes:
    • 22 pairs are autosomes
    • 1 pair is sex chromosomes:
      • Female: XX
      • Male: XY

🧬 Types of Sex-Linked Inheritance

  1. X-linked Inheritance
    (Gene is on the X chromosome)
  2. Y-linked Inheritance
    (Gene is on the Y chromosome – also called holandric inheritance)

1️⃣ X-Linked Inheritance

Since females have two X chromosomes (XX) and males have one X and one Y (XY):

  • Males are more likely to express X-linked recessive conditions because they have only one X.
  • Females can be carriers if only one X carries the gene.

🔵 X-Linked Recessive Inheritance

  • The defective gene is on the X chromosome.
  • More common in males.
  • Carrier mothers have a 50% chance of passing the trait to sons (who will be affected) and daughters (who may become carriers).

🧬 Examples:

  • Hemophilia A (deficiency of clotting factor VIII)
  • Duchenne Muscular Dystrophy
  • Color blindness
  • G6PD deficiency

🧪 Cross Example:

Carrier Mother (XᴴX) × Normal Father (XY)

ChildGenotypePhenotype
DaughterXᴴXCarrier
DaughterXXNormal
SonXᴴYAffected
SonXYNormal

🔴 X-Linked Dominant Inheritance

  • Only one defective X allele is enough to cause the disorder in both males and females.
  • Affected fathers will pass the condition to all daughters (because daughters get the father’s X), but none of the sons.
  • Affected mothers can pass it to both sons and daughters.

🧬 Examples:

  • Rett syndrome
  • Fragile X syndrome

2️⃣ Y-Linked Inheritance (Holandric)

  • Gene is located on the Y chromosome.
  • Only males are affected.
  • Passed from father to son.
  • Very rare because the Y chromosome has few genes.

🧬 Examples:

  • Y-linked male infertility
  • Swyer syndrome (defective SRY gene)

📊 Comparison Table: X-linked vs Y-linked Inheritance

FeatureX-Linked RecessiveX-Linked DominantY-Linked
Affected MalesCommonLess commonOnly males
Affected FemalesRareCommonNever
Carrier FemalePossibleNot applicableNot applicable
Father → Son❌ (X comes from mother)
Father → Daughter

🧑‍⚕️ Nursing Relevance of Sex-Linked Inheritance

AreaApplication
Genetic CounselingExplaining risk of inherited disorders based on sex.
Prenatal ScreeningDetecting X-linked disorders in male fetuses.
Patient EducationHelping families understand carrier status and inheritance patterns.
Hemophilia ManagementTeaching injection of clotting factors and bleeding precautions.
Ethical SupportRespecting family decisions in genetic testing and reproduction.

Key Takeaways

  • Sex-linked traits are carried on X or Y chromosomes.
  • X-linked recessive disorders often affect males, females are carriers.
  • Y-linked traits affect only males and are passed from father to son.
  • Nurses play a key role in identifying, educating, and supporting families affected by genetic disorders.

🧬 Mechanism of Inheritance


🧾 Definition

The mechanism of inheritance refers to how genetic traits and characteristics are passed from parents to offspring through genes located on chromosomes.

Inheritance follows the rules of Mendelian and non-Mendelian genetics, involving DNA, genes, chromosomes, and the processes of replication, transcription, translation, and cell division.


🔗 Basic Components of Inheritance

ComponentDescription
DNADeoxyribonucleic acid – the genetic material
GenesSegments of DNA that carry instructions for traits
ChromosomesStructures made of DNA that contain genes
AllelesDifferent forms of a gene (dominant or recessive)
GametesSperm and egg cells that carry genetic information
ZygoteFertilized egg formed by union of sperm and ovum

🔄 Steps in the Mechanism of Inheritance

1️⃣ Gene Transmission through Gametes

  • During meiosis, gametes (sperm and ovum) are formed.
  • Each gamete carries one set of chromosomes (haploid = n).
  • At fertilization, the egg and sperm fuse to form a zygote (diploid = 2n).
  • Each parent contributes half of the genetic material.

2️⃣ Chromosomal Basis of Inheritance

  • Humans have 23 pairs of chromosomes (46 total).
    • 22 pairs of autosomes
    • 1 pair of sex chromosomes (XX or XY)
  • Genes are located at specific loci (positions) on chromosomes.
  • Traits are inherited based on the arrangement and pairing of these genes.

3️⃣ Expression of Traits

  • Genes are expressed via protein synthesis:
    • Transcription: DNA → mRNA (in nucleus)
    • Translation: mRNA → Protein (in ribosome)
  • These proteins determine phenotypes (observable traits), such as eye color, height, or blood type.

4️⃣ Mendelian Inheritance Patterns

  • Law of Segregation: Each parent passes one of two alleles to the offspring.
  • Law of Independent Assortment: Genes for different traits are passed independently.
  • Law of Dominance: Dominant alleles mask recessive ones.

5️⃣ Non-Mendelian Inheritance (Special Cases)

  • Incomplete dominance: Blending of traits (e.g., red + white = pink flowers)
  • Co-dominance: Both alleles are expressed equally (e.g., AB blood group)
  • Multiple alleles: More than two allele options exist (e.g., ABO system)
  • Polygenic traits: Controlled by multiple genes (e.g., height, skin color)
  • Sex-linked inheritance: Traits linked to sex chromosomes (e.g., hemophilia)

🧬 Genotype vs. Phenotype

TermDescriptionExample
GenotypeGenetic makeup (alleles present)AA, Aa, aa
PhenotypeObservable trait or appearanceTall, Short

🧑‍⚕️ Relevance in Nursing Practice

Application AreaImportance
Genetic CounselingHelps explain inheritance risks and patterns
Prenatal DiagnosisDetects inherited diseases early
Personalized MedicineTreatments based on individual genetic makeup
Pediatric CareManaging inherited conditions like thalassemia
Patient EducationExplaining dominant/recessive traits in simple terms

Summary

  • Inheritance occurs through genes located on chromosomes.
  • Gametes carry genetic information; fusion during fertilization passes traits to the offspring.
  • Traits are expressed depending on dominant/recessive alleles.
  • Inheritance follows Mendelian or non-Mendelian patterns.
  • Nurses must understand inheritance to assist in diagnosis, counseling, and education.

🧬 Errors in Transmission – Mutation


🧾 Definition

A mutation is a permanent change in the DNA sequence of a gene or chromosome. It is an error in the transmission of genetic information from one generation to the next or during cell division.

Mutations can:

  • Occur spontaneously
  • Be inherited
  • Be caused by external factors (e.g., radiation, chemicals, viruses)

⚙️ Mechanism of Mutation (Error in Transmission)

🧬 When do mutations occur?

  • During DNA replication (cell division)
  • During meiosis (formation of sperm or egg)
  • By environmental mutagens (radiation, drugs)

These errors may:

  • Affect one gene (gene mutation)
  • Affect chromosomal structure or number (chromosomal mutation)

🔬 Types of Mutations

🔹 1. Gene (Point) Mutations

Change in the DNA sequence of a single gene.

TypeDescriptionExample
SubstitutionOne base is replaced by anotherSickle cell anemia (A → T substitution in beta-globin gene)
InsertionExtra base is addedFrameshift mutation
DeletionA base is removedCystic fibrosis (deletion of 3 bases)

🔸 2. Chromosomal Mutations

Changes in number or structure of chromosomes.

TypeDescriptionExample
DeletionA part of chromosome is missingCri-du-chat syndrome
DuplicationRepetition of a chromosome segmentSome developmental delays
InversionSegment flips and reinsertsMay cause miscarriages
TranslocationSegment moves to another chromosomeSome cases of Down syndrome (Robertsonian translocation)

🔹 3. Numerical Mutations (Aneuploidy)

Incorrect number of chromosomes due to non-disjunction during meiosis.

ConditionChromosome InvolvedFeatures
Down SyndromeTrisomy 21Intellectual disability, flat facial features
Turner SyndromeXOShort stature, infertility in females
Klinefelter SyndromeXXYMale with low testosterone, infertility

🚫 Causes of Mutations (Mutagens)

MutagenSource
RadiationX-rays, UV rays
ChemicalsCigarette smoke, pesticides, drugs
VirusesHPV (linked to cervical cancer)
Errors in replicationSpontaneous DNA mistakes

📊 Effects of Mutations

EffectResult
Silent mutationNo change in protein function
Missense mutationAlters protein (may be harmful or beneficial)
Nonsense mutationStops protein formation prematurely
Frameshift mutationChanges the reading frame, often severe

🧑‍⚕️ Nursing Relevance and Responsibilities

AreaNurse’s Role
Prenatal CareAssist with genetic screening (e.g., amniocentesis)
EducationTeach families about inherited risks and genetic testing
Newborn ScreeningEarly detection of conditions like PKU or hypothyroidism
Genetic CounselingSupport families facing inherited disorders
Oncology CareSome cancers are caused by genetic mutations (e.g., BRCA in breast cancer)

Key Takeaways

  • Mutations are errors in gene or chromosome structure/number.
  • They may be harmless, beneficial, or harmful.
  • Can cause genetic disorders, cancers, or developmental abnormalities.
  • Nurses must be aware of mutation-related conditions, assist in screening, and provide emotional support and education.
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Categorized as BSC SEM 4 PATHOLOGY 2 & GENETICS, Uncategorised